Spontaneous regression of congenital cutaneous histiocytosis x: Report of a case with discussion of nosology and pathogenesis

Louis P. Dehner, Joel T. Bamford, Edward C. Mcdonald

Research output: Contribution to journalArticle

17 Citations (Scopus)

Abstract

Spontaneous regression of histiocytosis X is a rare biologic event as judged by the extensive recorded experience in the literature. We present a case of congenital cutaneous histiocytosis X that resolved without specific therapy in the first week of life. Histologic and ultrastructural studies confirmed the interpretation. This child is an example of so-called pure cutaneous histiocytosis, which, like the other unisystem forms of the disorders, has an excellent prognosis..

Original languageEnglish (US)
Pages (from-to)99-106
Number of pages8
JournalFetal and Pediatric Pathology
Volume1
Issue number1
DOIs
StatePublished - Jan 1 1983

Fingerprint

Histiocytosis
Langerhans Cell Histiocytosis
Skin
Therapeutics

Keywords

  • Birbeck granules
  • Histiocytosis X
  • Langerhans cells
  • Skin

Cite this

Spontaneous regression of congenital cutaneous histiocytosis x : Report of a case with discussion of nosology and pathogenesis. / Dehner, Louis P.; Bamford, Joel T.; Mcdonald, Edward C.

In: Fetal and Pediatric Pathology, Vol. 1, No. 1, 01.01.1983, p. 99-106.

Research output: Contribution to journalArticle

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