Ross-Konno and endocardial fibroelastosis resection after hybrid stage i palliation in infancy: Successful staged left-ventricular rehabilitation and conversion to biventricular circulation after fetal diagnosis of aortic stenosis

Anita J. Moon-Grady, Phillip Moore, Anthony Azakie

Research output: Contribution to journalArticlepeer-review

9 Scopus citations

Abstract

We report a patient who presented during fetal life with severe aortic stenosis, left-ventricular dysfunction, and endocardial fibroelastosis (evolving hypoplastic left heart syndrome). Management involved in utero and postnatal balloon aortic valvuloplasty for partial relief of obstruction and early postnatal hybrid stage I palliation until recovery of left-ventricular systolic function had occurred. The infant subsequently had successful conversion to a biventricular circulation by combining resection of endocardial fibroelastosis with single-stage Ross-Konno, aortic arch reconstruction, hybrid takedown, and pulmonary artery reconstruction.

Original languageEnglish (US)
Pages (from-to)211-214
Number of pages4
JournalPediatric Cardiology
Volume32
Issue number2
DOIs
StatePublished - Feb 2011

Keywords

  • Aortic stenosis
  • Fetal balloon aortic valvuloplasty
  • Fetal intervention
  • Hypoplastic left heart syndrome
  • Resection of endocardial fibroelastosis
  • Stage 1 hybrid

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