Progressive cardiac conduction defect and cardiomyopathy in siblings with syncope

Bradley P. Fuhrman, John L. Bass, Cheryl Lawrence, Russell V. Lucas

Research output: Contribution to journalArticlepeer-review

2 Scopus citations

Abstract

Three siblings evaluated for syncope were found to have left bundle-branch block. Progression to complete heart block occurred in all. Pacemaker implantation eliminated syncopal episodes in each case. Echocardiographic manifestations of cardiomyopathy were present in each child despite normal roentgenographic heart size. Careful family study identified no other affected members with conduction defects. These children are believed to represent a form of familial cardiomyopathy in which clinical manifestations of cardiac conduction system disease predominate.

Original languageEnglish (US)
Pages (from-to)57-62
Number of pages6
JournalPediatric Cardiology
Volume2
Issue number1
DOIs
StatePublished - Mar 1982

Keywords

  • Cardiomyopathy
  • Complete heart block
  • Familial progressive cardiac conduction defect
  • Left bundle-branch block
  • Syncope

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