Progressive cardiac conduction defect and cardiomyopathy in siblings with syncope

Bradley P. Fuhrman; John L. Bass; Cheryl Lawrence; Russell V. Lucas

doi:10.1007/BF02265618

Progressive cardiac conduction defect and cardiomyopathy in siblings with syncope

Bradley P. Fuhrman, John L. Bass, Cheryl Lawrence, Russell V. Lucas

Pediatric Cardiology

Research output: Contribution to journal › Article › peer-review

3 Scopus citations

Abstract

Three siblings evaluated for syncope were found to have left bundle-branch block. Progression to complete heart block occurred in all. Pacemaker implantation eliminated syncopal episodes in each case. Echocardiographic manifestations of cardiomyopathy were present in each child despite normal roentgenographic heart size. Careful family study identified no other affected members with conduction defects. These children are believed to represent a form of familial cardiomyopathy in which clinical manifestations of cardiac conduction system disease predominate.

Original language	English (US)
Pages (from-to)	57-62
Number of pages	6
Journal	Pediatric Cardiology
Volume	2
Issue number	1
DOIs	https://doi.org/10.1007/BF02265618
State	Published - Mar 1982

Keywords

Cardiomyopathy
Complete heart block
Familial progressive cardiac conduction defect
Left bundle-branch block
Syncope

Publisher link

10.1007/BF02265618

Find It

Find It at U of M Libraries

Cite this

@article{633c9eb4d38a403e83ef3b11c5517a45,

title = "Progressive cardiac conduction defect and cardiomyopathy in siblings with syncope",

abstract = "Three siblings evaluated for syncope were found to have left bundle-branch block. Progression to complete heart block occurred in all. Pacemaker implantation eliminated syncopal episodes in each case. Echocardiographic manifestations of cardiomyopathy were present in each child despite normal roentgenographic heart size. Careful family study identified no other affected members with conduction defects. These children are believed to represent a form of familial cardiomyopathy in which clinical manifestations of cardiac conduction system disease predominate.",

keywords = "Cardiomyopathy, Complete heart block, Familial progressive cardiac conduction defect, Left bundle-branch block, Syncope",

author = "Fuhrman, {Bradley P.} and Bass, {John L.} and Cheryl Lawrence and Lucas, {Russell V.}",

year = "1982",

month = mar,

doi = "10.1007/BF02265618",

language = "English (US)",

volume = "2",

pages = "57--62",

journal = "Pediatric Cardiology",

issn = "0172-0643",

publisher = "Springer New York",

number = "1",

}

TY - JOUR

T1 - Progressive cardiac conduction defect and cardiomyopathy in siblings with syncope

AU - Fuhrman, Bradley P.

AU - Bass, John L.

AU - Lawrence, Cheryl

AU - Lucas, Russell V.

PY - 1982/3

Y1 - 1982/3

N2 - Three siblings evaluated for syncope were found to have left bundle-branch block. Progression to complete heart block occurred in all. Pacemaker implantation eliminated syncopal episodes in each case. Echocardiographic manifestations of cardiomyopathy were present in each child despite normal roentgenographic heart size. Careful family study identified no other affected members with conduction defects. These children are believed to represent a form of familial cardiomyopathy in which clinical manifestations of cardiac conduction system disease predominate.

AB - Three siblings evaluated for syncope were found to have left bundle-branch block. Progression to complete heart block occurred in all. Pacemaker implantation eliminated syncopal episodes in each case. Echocardiographic manifestations of cardiomyopathy were present in each child despite normal roentgenographic heart size. Careful family study identified no other affected members with conduction defects. These children are believed to represent a form of familial cardiomyopathy in which clinical manifestations of cardiac conduction system disease predominate.

KW - Cardiomyopathy

KW - Complete heart block

KW - Familial progressive cardiac conduction defect

KW - Left bundle-branch block

KW - Syncope

UR - http://www.scopus.com/inward/record.url?scp=0020472643&partnerID=8YFLogxK

UR - http://www.scopus.com/inward/citedby.url?scp=0020472643&partnerID=8YFLogxK

U2 - 10.1007/BF02265618

DO - 10.1007/BF02265618

M3 - Article

C2 - 7063429

AN - SCOPUS:0020472643

SN - 0172-0643

VL - 2

SP - 57

EP - 62

JO - Pediatric Cardiology

JF - Pediatric Cardiology

IS - 1

ER -

Progressive cardiac conduction defect and cardiomyopathy in siblings with syncope

Abstract

Keywords

Publisher link

Find It

Other files and links

Fingerprint

Cite this