Primary pulmonary angiosarcoma: case reports and review of the literature

Mayur Virarkar, Sidra Tayyab, Rajesh Thampy, Priya Bhosale, Chitra Viswanathan

Research output: Contribution to journalReview articlepeer-review

3 Scopus citations


Pulmonary artery angiosarcoma is a rare malignant vascular tumor with an aggressive clinical course and a poor prognosis. Hemoptysis and shortness of breath have been reported as common clinical presentations. The exact clinicopathology is unknown. A tissue specimen obtained by percutaneous fine-needle aspiration cytology or open/thoracoscopic biopsy can confirm the diagnosis based on histopathological and immunohistochemical features. The differential diagnosis includes pulmonary thromboembolism, vascular malformations, and lung carcinoma. There is a paucity of literature describing this tumor, with only a few case reports available. There is also a lack of standardized guidelines for management, which further worsens the survival outcome. We report 3 cases of pulmonary artery angiosarcoma and review the recent literature.

Original languageEnglish (US)
Pages (from-to)347-352
Number of pages6
JournalAsian Cardiovascular and Thoracic Annals
Issue number5
StatePublished - Jun 1 2019
Externally publishedYes

Bibliographical note

Publisher Copyright:
© The Author(s) 2019.


  • Diagnosis
  • differential
  • hemangiosarcoma
  • immunohistochemistry
  • mediastinal neoplasms
  • pulmonary artery
  • vascular neoplasms


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