Pierre Robin Sequence

Sun T. Hsieh, Albert S. Woo

Research output: Contribution to journalReview articlepeer-review

5 Scopus citations

Abstract

Pierre Robin sequence consists of clinical triad of micrognathia, glossoptosis, and airway compromise with variable inclusion of cleft palate. Evaluation of airway obstruction includes physical examination, polysomnography for obstruction events, and a combination of nasoendoscopy and bronchoscopy to search for synchronous obstructive lesions. A multidisciplinary approach is required given the high rate of syndromic disease. Management of airway obstruction and feeding starts with nonsurgical maneuvers, such as prone and lateral positioning, nasopharyngeal stenting, and continuous positive airway pressure. Surgical management includes mandibular distraction and tongue-lip adhesion. Subglottic obstruction and central sleep apnea may best be treated with tracheostomy.

Original languageEnglish (US)
Pages (from-to)249-259
Number of pages11
JournalClinics in Plastic Surgery
Volume46
Issue number2
DOIs
StatePublished - Apr 2019
Externally publishedYes

Keywords

  • Cleft palate
  • Distraction
  • Glossoptosis
  • Micrognathia
  • Pierre Robin sequence

PubMed: MeSH publication types

  • Journal Article
  • Review

Fingerprint Dive into the research topics of 'Pierre Robin Sequence'. Together they form a unique fingerprint.

Cite this