Abstract
We report the ninth case of plexiform neurofibroma of the larynx, which occurred in a 2-year-old with multiple café au lait spots and obstructive sleep apnea. In discussing this clinical problem, we have attempted to make the following points. 1 A patient's having more than six café au lait spots of greater than 1.5-cm diameter is diagnostic of von Recklinghausen's disease. 2 It is much more difficult to completely excise plexiform neurofibroma than nonplexiform neurofibroma. 3 The association of juvenile xanthogranuloma with von Recklinghausen's disease may be a risk factor for the later development of leukemia.
| Original language | English (US) |
|---|---|
| Pages (from-to) | 53-55 |
| Number of pages | 3 |
| Journal | Annals of Otology, Rhinology & Laryngology |
| Volume | 96 |
| Issue number | 1 |
| DOIs | |
| State | Published - Jan 1987 |
| Externally published | Yes |
Keywords
- laryngeal neurofibroma
- laryngeal tumor
- neurofibromatosis
- plexiform neurofibroma
- von Recklinghausen's disease
- xanthogranuloma