Late-onset pulmonary arterial hypertension in repaired D-transposition of great arteries: An uncommon complication

Janani Baskaran, Kimara S. March, Thenappan Thenappan

Research output: Contribution to journalArticlepeer-review

1 Scopus citations

Abstract

Late-onset pulmonary arterial hypertension (PAH) is a rare but fatal complication in patients with childhood surgical repair of dextro-transposition of great arteries (D-TGA), especially with the Mustard and Senning procedures. The pathogenic mechanisms of PAH in patients with repaired D-TGA are not well understood and treatment is not standardized. In this manuscript, we present a case of late-onset PAH in an adult D-TGA patient after Mustard repair and discuss the pathogenic mechanisms, diagnosis, and treatment of pulmonary hypertension in repaired D-TGA.

Original languageEnglish (US)
Pages (from-to)547-550
Number of pages4
JournalPulmonary Circulation
Volume7
Issue number2
DOIs
StatePublished - 2017

Bibliographical note

Funding Information:
TT was funded by an AHA Scientist Development Grant 15SDG25560048 and a Lillehei Heart Institute High Risk and High Reward Grant.

Keywords

  • Baffle
  • Congenital
  • Cyanotic
  • Mustard
  • Right ventricle

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