Hereditary Proximal Spinal and Bulbar Motor Neuron Disease of Late Onset: A Report of Six Cases

Keyphrases

• Motor Neuron Disease 100%
• Late-onset 100%
• Bulbar 100%
• Type 1 Diabetes Mellitus (T1DM) 33%
• Diabetes 33%
• Genetic Counseling 33%
• Progressive Disease 33%
• Slow Progression 33%
• Adult-onset 33%
• Electromyography 33%
• Slowly Progressive 33%
• Muscle Biopsy 33%
• Supportive Therapy 33%
• Severe Disabilities 33%
• Tongue 33%
• Furrow 33%
• Reassurance 33%
• Gynecomastia 33%
• Proximal muscles 33%
• Fiber-type Grouping 33%
• Pyramidal Tract 33%
• X-linked Inheritance 33%
• Periodic Inspection 33%
• Muscle Involvement 33%
• Type 1 Fiber Predominance 33%
• Neurogenic Change 33%
• Bulbar muscles 33%

Medicine and Dentistry

• Motor Neuron Disease 100%
• Disease 33%
• Diabetes 33%
• Diabetes Mellitus 33%
• Tongue 33%
• Muscle Biopsy 33%
• Electromyography 33%
• Reassurance 33%
• Genetic Counseling 33%
• Gynecomastia 33%
• Pyramidal Sign 33%