Hepatic lymphangiomatosis mimicking polycystic liver disease

Deirdre A. O'Sullivan, Vicente E. Torres, Piet C. De Groen, Kenneth P. Baits, Bernard F. King, Jerry Vockley

Research output: Contribution to journalArticlepeer-review

30 Scopus citations


Hepatic lymphangiomatosis is a rare disorder characterized by cystic dilatation of the lymphatic vessels in the hepatic parenchyma. It can occur in the liver alone, in the liver and spleen, or in multiple organs. Clinically, diagnosis can be difficult because of the rarity and protean manifestations of this disorder. We describe a 53-year-old woman with hepatic lymphangiomatosis in whom polycystic liver disease had been previously diagnosed. In addition, we review 12 cases of hepatic, splenic, and hepatosplenic lymphangiomatosis with or without systemic lymphangiomatosis and discuss the differential diagnosis.

Original languageEnglish (US)
Pages (from-to)1188-1192
Number of pages5
JournalMayo Clinic Proceedings
Issue number12
StatePublished - 1998
Externally publishedYes


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