Headaches as a presenting symptom of linear morphea en coup de sabre

Ingrid Polcari, Amanda Moon, Erin F. Mathes, Elaine S. Gilmore, Amy S. Paller

Research output: Contribution to journalArticlepeer-review

19 Scopus citations


Linear morphea en coup de sabre (ECDS) is a form of localized scleroderma that predominantly affects the pediatric population, with a median age of 10 years at presentation. The existence of neurologic findings in association with ECDS has been well described in the literature. Here we describe 4 patients with ECDS who presented with headaches, which were typical migraines in 3 of the patients. The headaches preceded the onset of cutaneous findings by at least 6 months. Our patients' cases emphasize both the importance of recognizing headaches as a harbinger of ECDS and the necessity of performing thorough cutaneous examination in patients with unexplained headaches or other neurologic disease.

Original languageEnglish (US)
Pages (from-to)e1715-e1719
Issue number6
StatePublished - Dec 1 2014

Bibliographical note

Publisher Copyright:
Copyright © 2014 by the American Academy of Pediatrics.


  • Children
  • Female
  • Humans
  • Localized/complications
  • Localized/drug therapy
  • Localized/pathology
  • Male
  • Migraine headache
  • Neurologic
  • Scalp dermatoses/complications
  • Scalp dermatoses/drug therapy
  • Scalp dermatoses/pathology
  • Scleroderma
  • Scleroderma
  • Scleroderma


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