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Erdj3 Has an Essential Role for Z Variant Alpha-1-Antitrypsin Degradation
Nazli Khodayari
, George Marek
, Yuanqing Lu
, Karina Krotova
, Rejean Liqun Wang
, Mark Brantly
The Hormel Institute
Research output
:
Contribution to journal
›
Article
›
peer-review
20
Scopus citations
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Dive into the research topics of 'Erdj3 Has an Essential Role for Z Variant Alpha-1-Antitrypsin Degradation'. Together they form a unique fingerprint.
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Keyphrases
Alpha-1 Antitrypsin
100%
ERdj3
100%
Variants α
100%
Endoplasmic Reticulum
66%
Alpha-1 Antitrypsin Deficiency
50%
Hepatocytes
33%
Autophagy
33%
Liver Disease
33%
Toxic Gain of Function
33%
Amino Acids
16%
Quality Control
16%
Interacting Proteins
16%
Emphysema
16%
Family Members
16%
Traffic Network
16%
Monocytes
16%
Misfolding
16%
Calreticulin
16%
Inherited Disease
16%
Single Amino Acid Substitution
16%
New Therapeutic Approaches
16%
Endoplasmic Reticulum-associated Degradation
16%
Autophagosome Formation
16%
Hsp40
16%
Huh7.5 Cells
16%
EDEM1
16%
Co-immunoprecipitation (co-IP)
16%
Pharmacology, Toxicology and Pharmaceutical Science
Alpha 1 Antitrypsin
100%
Alpha 1 Antitrypsin Deficiency
60%
Amino Acid
40%
Liver Disease
40%
Immunoprecipitation
20%
Genetic Disorder
20%
Emphysema
20%
Heat Shock Protein 40
20%
Calreticulin
20%
Biochemistry, Genetics and Molecular Biology
Alpha 1-Antitrypsin
100%
Deficiency
37%
Hepatocyte
25%
Autophagy
25%
Quality Control
12%
Amino Acids
12%
Immunoprecipitation
12%
Genetic Disorder
12%
Endoplasmic-Reticulum-Associated Protein Degradation
12%
Amino Acid Substitution
12%
Autophagosome
12%
Calreticulin
12%
Immunology and Microbiology
Alpha 1-Antitrypsin
100%
Endoplasmic reticulum
50%
Autophagy
25%
Cell Line
12%
Autophagosome
12%
Immunoprecipitation
12%
Amino Acid Substitution
12%
Endoplasmic Reticulum Associated Degradation
12%
Calreticulin
12%
Amino Acid
12%