Embryonal adenoma of the kidney associated with polycythemia and von Willebrand disease

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Abstract

Purpose: We studied the significance, identification and management of acquired von Willebrand disease and polycythemia associated with benign renal tumors in children. Materials and Methods: Two patients who presented with polycythemia and a renal mass were also found to have acquired von Willebrand disease. One patient was treated with radical nephrectomy and 1 was treated with partial nephrectomy. The patients have been followed for 19 and 10 months, respectively. Results: Excision of the renal mass resulted in prompt resolution of polycythemia and von Willebrand disease in each patient. Perioperatively 1-deamino-(8-D-arginine)-vasopressin was given to control bleeding. Each patient had benign embryonal adenoma of the kidney. Conclusions: Polycythemia and von Willebrand disease may be associated with benign kidney neoplasms. Children and adolescents with a renal mass may benefit from preoperative screening for coagulopathy.

Original languageEnglish (US)
Pages (from-to)2171-2174
Number of pages4
JournalJournal of Urology
Volume160
Issue number6 I
DOIs
StatePublished - Jan 1 1998

Keywords

  • Kidney
  • Nephrectomy
  • Polycythemia
  • Von Willebrand's disease

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