Congenital unilateral pulmonary venous atresia with pulmonary veno-occlusive disease in contralateral lung: An unusual association

Savitri Shrivastava, James H Moller, Jesse E. Edwards

Research output: Contribution to journalArticlepeer-review

13 Scopus citations

Abstract

A patient presenting with the rare association of congenital unilateral pulmonary venous atresia in one lung and pulmonary veno-occlusive disease in the other is described. The patient first presented at the age of 3 1/2 years with anemia, hemoptysis, and pulmonary hypertension. After cardiac catheterization and angiocardiography, a diagnosis of atresia of the left pulmonary veins was made for which left pneumonectomy was done. Four years later the patient presented with right-sided congestive failure and radiologic evidence of right-sided pulmonary edema from which death resulted. At autopsy, the right lung showed changes of pulmonary veno-occlusive disease, while the major veins were not involved.

Original languageEnglish (US)
Pages (from-to)213-219
Number of pages7
JournalPediatric Cardiology
Volume7
Issue number4
DOIs
StatePublished - Dec 1 1986

Keywords

  • Pulmonary hypertension
  • Pulmonary venous hypertension
  • Pulmonary venous obstruction

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