Congenital extensive central venous thrombosis with chylous ascites and chylothoraces

Ramnik Patel, Massimo Griselli, A. M. Barrett

Research output: Contribution to journalArticlepeer-review

8 Scopus citations

Abstract

We describe a case of congenital extensive central venous thrombosis presenting as polyhydramnios and massive ascites, requiring amnioreduction prenatally and refractory chylous ascites and chylothoraces postnatally. Echocardiography, computed tomography angiogram (CTA), and magnetic resonance venogram (MRV) were helpful in defining the nature and extent of the lesion. The patient underwent staged procedures of repeated abdominal paracentesis, chest drain insertion, and right internal jugular vein exploration initially. Subsequently, open thromboembolectomy from the upper venous system veins and pericardial patch angioplasty of the right internal jugular and right innominate veins were required and managed by catheter-directed thrombolysis for the residual thrombosis with successful recovery.

Original languageEnglish (US)
Pages (from-to)E5-E8
JournalJournal of Pediatric Surgery
Volume48
Issue number2
DOIs
StatePublished - Feb 2013
Externally publishedYes

Keywords

  • Chylothorax
  • Chylous ascites
  • Congenital venous thrombosis
  • Factor V Leiden mutation

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