Cardiac Transplantation Does Not Improve Exercise Tolerance, Muscle Mass, or Substrate Metabolism in Barth Syndrome

Keyphrases

• 31P-MRS 5%
• ATP Production 5%
• Barth Syndrome 100%
• Body Composition Analysis 5%
• Cardiac Transplantation 100%
• Cardiomyopathy 5%
• Echocardiography 5%
• Exercise Capacity 5%
• Exercise Intolerance 11%
• Exercise Tolerance 100%
• Fat-free Mass 5%
• Graded Exercise Testing 5%
• Growth Delay 5%
• Healthy Controls 17%
• Heart Function 11%
• Heart Rate Response 5%
• Low Heart Rate 5%
• Metabolic Abnormalities 11%
• Metabolic Consequences 5%
• Metabolic Effects 5%
• Metabolism Study 5%
• Mitochondrial Dysfunction 5%
• Mitochondrial Energetics 5%
• Muscle Mass 100%
• Neutropenia 5%
• No Significant Difference 5%
• Phosphocreatine Recovery 5%
• Plasma Lactate 5%
• Skeletal Morphology 5%
• Skeletal muscle Bioenergetics 11%
• Skeletal muscle Mass 5%
• Substrate Metabolism 100%
• Tafazzin 5%
• Targeted Therapy 5%
• Transplantation 5%
• VO2peak 5%
• X-linked Disorder 5%

Biochemistry, Genetics and Molecular Biology

• 31P NMR Spectroscopy 25%
• Adenosine Triphosphate 25%
• Body Composition 25%
• Energy Transfer 100%
• Exercise Tolerance 100%
• Fat Free Mass 25%
• Heart Function 50%
• Lactate Blood Level 25%
• Metabolic Pathway 100%
• Mitochondrial Disorder 25%
• Skeletal Muscle 75%
• Targeted Therapy 25%

Medicine and Dentistry

• Adenosine Triphosphate 5%
• Barth Syndrome 100%
• Creatine Phosphate 5%
• Diseases 5%
• Echocardiography 5%
• Energy Transfer 17%
• Exercise Intolerance 11%
• Exercise Test 5%
• Exercise Tolerance 100%
• Heart Function 11%
• Heart Transplantation 100%
• Lactic Acid 5%
• Mitochondrial Disorder 5%
• Muscle Energetics 5%
• Myopathy 5%
• Neutropenia 5%
• Phosphorus Nuclear Magnetic Resonance 5%
• Skeletal Muscle 17%
• Targeted Therapy 5%