An unusual presentation of immunoglobulin A gammopathy in a patient with Schnitzler's syndrome

Elizabeth Kaganov, Divita Jhaveri, Peter Peters, Jacob W. IJdo

Research output: Contribution to journalArticlepeer-review

1 Scopus citations

Abstract

This case summarizes a 69-year-old woman who presented with a history of recurrent fevers, widespread urticarial rash and generalized myalgias for several years with an eventual diagnosis of Schnitzler's syndrome. This is a rare autoinflammatory condition which typically involves a chronic urticarial rash, monoclonal immunoglobulin M (IgM) or IgG gammopathy. Rapid improvement in above symptoms were noted with anakinra, an interleukin-1 receptor antagonist. We report an unusual case of a 69-year-old woman who presented with an isolated IgA monoclonal gammopathy.

Original languageEnglish (US)
Pages (from-to)2085-2088
Number of pages4
JournalInternational Journal of Rheumatic Diseases
Volume26
Issue number10
DOIs
StatePublished - Oct 2023
Externally publishedYes

Bibliographical note

Publisher Copyright:
© 2023 The Authors. International Journal of Rheumatic Diseases published by Asia Pacific League of Associations for Rheumatology and John Wiley & Sons Australia, Ltd.

Keywords

  • IL-1 receptor antagonist
  • IgA gammopathy
  • Schnitzler's syndrome
  • Schnitzler-like syndromes
  • anakinra

PubMed: MeSH publication types

  • Case Reports

Fingerprint

Dive into the research topics of 'An unusual presentation of immunoglobulin A gammopathy in a patient with Schnitzler's syndrome'. Together they form a unique fingerprint.

Cite this